Glomerulocystic disease, a rare cause of renal cysts in infants: A series of three cases

dc.contributor.authorIslam, Nen_US
dc.contributor.authorMandal, Ben_US
dc.contributor.authorBera, Gen_US
dc.contributor.authorMukherjee, Sen_US
dc.contributor.authorChatterjee, Uen_US
dc.date.accessioned2020-04-10T01:49:48Z
dc.date.available2020-04-10T01:49:48Z
dc.date.issued2019-03
dc.description.abstractGlomerulocystic kidney disease (GCKD) is an uncommon type of cystic renal disease affecting children. It has both sporadic and familial occurrence and is characterized by cortical microcysts associated with dilatation of Bowman's spaces. In some instances, GCKD is an early manifestation of autosomal dominant polycystic kidney disease. Here, we present three cases of GCKD, two in infants and one in a perinatal postmortem. The first one is a case of GCKD with unilateral involvement, diagnosed on surgical biopsy. GCKD is a morphological expression of several hereditary and nonhereditary disorders that differ vastly in their management and long-term outcome. Hence, accurate morphological diagnosis of this entity is important for prognostication and genetic counseling.en_US
dc.identifier.affiliationsDepartment of Pathology, IPGME and R, Kolkata, West Bengal, Indiaen_US
dc.identifier.affiliationsDepartment of Neonatology, IPGME and R, Kolkata, West Bengal, Indiaen_US
dc.identifier.citationIslam N, Mandal B, Bera G, Mukherjee S, Chatterjee U. Glomerulocystic disease, a rare cause of renal cysts in infants: A series of three cases. Indian Journal of Pathology and Microbiology. 2019 Mar; 62(1): 95-98en_US
dc.identifier.issn0377-4929
dc.identifier.issn0974-5130
dc.identifier.placeIndiaen_US
dc.identifier.urihttps://imsear.searo.who.int/handle/123456789/196291
dc.languageenen_US
dc.publisherIndian Association of Pathologists and Microbiologistsen_US
dc.relation.issuenumber1en_US
dc.relation.volume62en_US
dc.source.urihttps://dx.doi.org/10.4103/IJPM.IJPM_643_17en_US
dc.subjectAutosomal dominant polycystic kidney diseaseen_US
dc.subjectglomerulocystic kidney diseaseen_US
dc.subjectpediatric renal cystsen_US
dc.titleGlomerulocystic disease, a rare cause of renal cysts in infants: A series of three casesen_US
dc.typeJournal Articleen_US
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