Glomerulocystic disease, a rare cause of renal cysts in infants: A series of three cases
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Date
2019-03
Journal Title
Journal ISSN
Volume Title
Publisher
Indian Association of Pathologists and Microbiologists
Abstract
Glomerulocystic kidney disease (GCKD) is an uncommon type of cystic renal disease affecting children. It has both sporadic and familial occurrence and is characterized by cortical microcysts associated with dilatation of Bowman's spaces. In some instances, GCKD is an early manifestation of autosomal dominant polycystic kidney disease. Here, we present three cases of GCKD, two in infants and one in a perinatal postmortem. The first one is a case of GCKD with unilateral involvement, diagnosed on surgical biopsy. GCKD is a morphological expression of several hereditary and nonhereditary disorders that differ vastly in their management and long-term outcome. Hence, accurate morphological diagnosis of this entity is important for prognostication and genetic counseling.
Description
Keywords
Autosomal dominant polycystic kidney disease, glomerulocystic kidney disease, pediatric renal cysts
Citation
Islam N, Mandal B, Bera G, Mukherjee S, Chatterjee U. Glomerulocystic disease, a rare cause of renal cysts in infants: A series of three cases. Indian Journal of Pathology and Microbiology. 2019 Mar; 62(1): 95-98