Partial expression of Papillon-Lefèvre Syndrome.

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dc.contributor.authorKothiwale, Shaila Ven_US
dc.contributor.authorMathur, Setuen_US
dc.date.accessioned2009-05-28T07:45:02Z
dc.date.available2009-05-28T07:45:02Z
dc.date.issued2008-07-18en_US
dc.description.abstractPapillon- Lefèvre Syndrome (PLS) is a rare autosomal recessive trait, which is transmitted with an estimated frequency of one to four per million individuals. It is characterized by palmar plantar keratosis and severe early-onset periodontitis affecting both deciduous and permanent dentition. In this report, we present clinical, microbiological and leukocyte function test findings of a thirty-five year-old patient with symptoms typical of Papillon-Lefèvre Syndrome except for premature loss of deciduous and permanent dentition. The patient exhibited palmar plantar keratosis and an isolated, moderately deep periodontal pocket in the third quadrant. No anaerobic bacteria were isolated from the plaque culture. The neutrophil function test revealed defective chemotaxis and phagocytosis while intracellular killing and respiratory burst were normal.en_US
dc.description.affiliationDepartment of Periodontics, KLES'S Institute of Dental Sciences, Belgaum, India. shailakothiwale2000@yahoo.comen_US
dc.identifier.citationKothiwale SV, Mathur S. Partial expression of Papillon-Lefèvre Syndrome. Indian Journal of Dental Research. 2008 Jul-Sep; 19(3): 264-6en_US
dc.identifier.urihttps://imsear.searo.who.int/handle/123456789/51615
dc.language.isoengen_US
dc.source.urihttps://www.ijdr.inen_US
dc.subject.meshAdulten_US
dc.subject.meshChemotaxis, Leukocyte --physiologyen_US
dc.subject.meshHumansen_US
dc.subject.meshKeratoderma, Palmoplantar --pathologyen_US
dc.subject.meshMaleen_US
dc.subject.meshNeutrophils --physiologyen_US
dc.subject.meshPapillon-Lefevre Disease --diagnosisen_US
dc.subject.meshPenetranceen_US
dc.subject.meshPeriodontal Pocket --pathologyen_US
dc.subject.meshPeriodontitis --pathologyen_US
dc.subject.meshPhagocytosis --physiologyen_US
dc.subject.meshTooth Exfoliation --pathologyen_US
dc.subject.meshTooth, Deciduous --pathologyen_US
dc.titlePartial expression of Papillon-Lefèvre Syndrome.en_US
dc.typeCase Reportsen_US
dc.typeJournal Articleen_US
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