EVAN’S SYNDROME – A RARE ENTITY
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Date
2024-07
Journal Title
Journal ISSN
Volume Title
Publisher
Era's Lucknow Medical College & Hospital, Lucknow in association with American University of Barbados (AUB)
Abstract
The Evans syndrome was first identified by Robert Evans in 1951. Primary thrombocytopenic purpura and acquired hemolytic anemia are r e l a t e d b y a r a r e a u t o i m m u n e d i s e a s e . I m m u n o l o g i c a l thrombocytopenia (ITP) and autoimmune hemolytic anemia (AIHA) may develop in this illness simultaneously or consecutively, and immunological neutropenia may also follow ITP. About 2–5% of ITP patients and 5–10% of warm autoimmune hemolytic anemia cases have Evans syndrome, which is often identified by exclusion. Our case report focuses on a female patient, age 15, who complained of anemia, jaundice, and petechiae. Her lab tests revealed higher amounts of reticulocytes, lactic dehydrogenase, positive Coomb's test, and indirect bilirubin. Due to the presence of thrombocytopenia and hemolytic anemia that tested positive for Coomb's, she was diagnosed with Evan's syndrome. There was no main autoimmune illness indicated by the negative ANA profile for SS-A. Evans syndrome can be hard to diagnose and treat. Corticosteroids and other immunosuppressive drugs are commonly used in treatment.
Description
Keywords
Evans syndrome, Autoimmune hemolytic anemia, Idiopathic thrombocytopenia.
Citation
Bano Beenish, Akther Mantasha, Sharma Priyanka, Shamim Faraz, Sharma Akanksha, Khan Farheen . EVAN’S SYNDROME – A RARE ENTITY. Era's Journal of Medical Research. 2024 Jul; 11(1): 139-142