Anesthesia for Pentalogy of Cantrell with Surgical Repair of Tetralogy of Fallot Along with Absent Diaphragm: A Case Study
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Date
2025-06
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Publisher
Wolters Kluwer – Medknow
Abstract
Pentalogy of Cantrell compiles the union of five anomalies including defects of the midline abdominal wall, lower sternum, anterior diaphragm, diaphragmatic pericardium, and any form of intra?cardiac pathology 1. The intra?cardiac defects associated commonly are ventricular septal defects, followed by atrial septal defects, Tetralogy of Fallot, and pulmonary stenosis 2. It is also a rare syndrome with an estimated incidence of 1:65,000 to 200,000 live births.3 4 Here in we present a case of a 4?year?old male patient, diagnosed with Pentalogy of Cantrel was referred to our institute with chief complaints of breathlessness associated with cyanosis on exertion. He has ectopia cordis along with omphalocele since birth.
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Keywords
Cyanosis, Omphalocele, Pentalogy of Cantrell, Tetralogy of Fallot
Citation
Maheshwari Vaibhav, Sahoo Manoranjan.Anesthesia for Pentalogy of Cantrell with Surgical Repair of Tetralogy of Fallot Along with Absent Diaphragm: A Case Study.Annals of Cardiac Anaesthesia.2025 Jun;28(2):181-183