Isolated intracranial Rosai Dorfman disease masquerading as meningioma: a case report.

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2007-04-22
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Abstract
Isolated intracranial Rosai Dorfman disease (sinus histiocytosis with massive lymphadenopathy) is rare. We present a 26-year-old male who presented with left focal motor seizures becoming secondarily generalized of one-year duration. Clinically and radiologically patient was diagnosed to have a right parietal convexity meningioma. However on histopathological examination a final diagnosis of intracranial Rosai Dorfman disease was rendered.
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Ghosal N, Murthy G, Visvanathan K, Sridhar M, Hegde AS. Isolated intracranial Rosai Dorfman disease masquerading as meningioma: a case report. Indian Journal of Pathology & Microbiology. 2007 Apr; 50(2): 382-4