Fahr’s disease: a rare degenerative disorder presenting with psychosis: a case report

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dc.contributor.authorSengupta, Soumiken_US
dc.contributor.authorNath, Subhashishen_US
dc.contributor.authorChetia, Dhrubajyotien_US
dc.contributor.authorDutta, Hemantaen_US
dc.date.accessioned2019-11-16T07:20:13Z
dc.date.available2019-11-16T07:20:13Z
dc.date.issued2014-07
dc.description.abstractBackground: Fahr’s syndrome (or Fahr’s disease) is a rare idiopathic degenerative disorder, characterized by bilateral symmetrical intracranial calcification and manifested as movement disorders, dementia and other behavioural disturbances. Case description: A 50-year-old male with long standing seizure disorder with intact motor and cognitive function presented with behavioural disturbances. Brain CT showed symmetrical calcification in cerebral hemispheres involving caudate nucleus, internal capsule, adjoining area and cerebellum. The history, clinical and radiological features and exclusion of other possibilities in our case point towards this uncommon disorder. Discussion: A substantial number of patients with Fahr‘s disease present with behavioural disturbances. Usually late onset Fahr’s disease with behavioural disturbances is accompanied by cognitive and motor abnormalities. However, in our case no such neurocognitive abnormalities were found along with the behavioural disturbances in the form of psychosis inspite of widespread intracranial calcification. Conclusion: Psychosis may be the sole presentation in a case of late onset Fahr‘s disease. Key message: Psychiatrist and Neurologist should remain vigilant regarding this uncommon presentation of this degenerative disease.en_US
dc.identifier.affiliationsAssistant Professor of Psychiatry, Department of Psychiatry, Lokoprio Gopinath Bordoloi Regional Institute of Mental Health, Tezpur, Indiaen_US
dc.identifier.affiliationsSenior Resident, Department of Psychiatry, Lokoprio Gopinath Bordoloi Regional Institute of Mental Health, Tezpur, Indiaen_US
dc.identifier.citationSengupta Soumik, Nath Subhashish, Chetia Dhrubajyoti, Dutta Hemanta. Fahr’s disease: a rare degenerative disorder presenting with psychosis: a case report. Andhra Pradesh Journal of Psychological Medicine. 2014 Jul-Dec; 15(2): 255-257en_US
dc.identifier.issn2249-5851
dc.identifier.placeIndiaen_US
dc.identifier.urihttps://imsear.searo.who.int/handle/123456789/183930
dc.languageenen_US
dc.publisherIndian Psychiatric Societyen_US
dc.relation.issuenumber2en_US
dc.relation.volume15en_US
dc.subjectFahr’s Diseaseen_US
dc.subjectDegenerative Disorderen_US
dc.subjectIntracranial Calcificationen_US
dc.subjectMovement Disorderen_US
dc.subjectPsychosisen_US
dc.titleFahr’s disease: a rare degenerative disorder presenting with psychosis: a case reporten_US
dc.typeJournal Articleen_US
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