Sporadic lymphangioleiomyomatosis with multiple atypical features: A case report and literature review
dc.contributor.author | Wang, X | en_US |
dc.contributor.author | Su, F | en_US |
dc.contributor.author | Zhou, F | en_US |
dc.contributor.author | Feng, M | en_US |
dc.date.accessioned | 2020-04-10T01:48:26Z | |
dc.date.available | 2020-04-10T01:48:26Z | |
dc.date.issued | 2018-03 | |
dc.description.abstract | Lymphangioleiomyomatosis (LAM) is a rare, genetically determined, progressive interstitial lung disease, which almost exclusively affects women, especially at the childbearing age. The initial symptoms and radiographic changes in a patient with LAM are always associated with the respiratory system. Here, we present a case of mediastinal and abdominal LAM of a 22-year-old male, where LAM cells are negative for human melanoma black-45 ( HMB-45). The report of this uncharacterized LAM case will make a significant contribution to the realization of LAM associated clinical features, diagnostic approaches, and its afterward treatments. | en_US |
dc.identifier.affiliations | Department of Oncology, Zhongnan Hospital of Wuhan University, Wuhan, Hubei, China | en_US |
dc.identifier.affiliations | Department of Oncology, The First Affiliated Hospital of Lanzhou University, Lanzhou, Gansu, China | en_US |
dc.identifier.citation | Wang X, Su F, Zhou F, Feng M. Sporadic lymphangioleiomyomatosis with multiple atypical features: A case report and literature review. Indian Journal of Pathology and Microbiology. 2018 Mar; 61(1): 94-97 | en_US |
dc.identifier.issn | 0377-4929 | |
dc.identifier.issn | 0974-5130 | |
dc.identifier.place | India | en_US |
dc.identifier.uri | https://imsear.searo.who.int/handle/123456789/196139 | |
dc.language | en | en_US |
dc.publisher | Indian Association of Pathologists and Microbiologists | en_US |
dc.relation.issuenumber | 1 | en_US |
dc.relation.volume | 61 | en_US |
dc.source.uri | https://dx.doi.org/10.4103/IJPM.IJPM_843_16 | en_US |
dc.subject | Extrapulmonary | en_US |
dc.subject | HMB-45 negative | en_US |
dc.subject | lymphangioleiomyomatosis | en_US |
dc.subject | man | en_US |
dc.title | Sporadic lymphangioleiomyomatosis with multiple atypical features: A case report and literature review | en_US |
dc.type | Journal Article | en_US |