Progressive bulbur paralysis (Fazio-Londe disease).

dc.contributor.authorGulati, Tarunaen_US
dc.contributor.authorDewan, Viveken_US
dc.contributor.authorKumar, Praveenen_US
dc.contributor.authorAhuja, Binaen_US
dc.contributor.authorAnand, V Ken_US
dc.date.accessioned2004-01-26en_US
dc.date.accessioned2009-05-30T16:03:34Z
dc.date.available2004-01-26en_US
dc.date.available2009-05-30T16:03:34Z
dc.date.issued2004-01-26en_US
dc.description.abstractProgressive bulbar paralysis of childhood is characterised by progressive paralysis of muscles innervated by cranial nerves. The authors report a case of progressive bulbar paralysis of childhood in a 12-year-old child. Child was admitted with the complaints of drooping of eyelids, difficulty in swallowing and hoarse voice. She had involvement of III, VII, IX, X, XI and XII cranial nerves and the corticospinal tracts. Electromyography revealed spontaneous activity in the form of fasciculations, giant motor unit potential and discrete recruitment of motor neurons suggestive of denervation pattern. Hearing assessment was normal. Muscle biopsy was also suggestive of neurogenic atrophy.en_US
dc.description.affiliationDepartment of Pediatrics Medicine, Kalawati Saran Children's Hospital and Lady Hardinge Medical College, New Delhi, India.en_US
dc.identifier.citationGulati T, Dewan V, Kumar P, Ahuja B, Anand VK. Progressive bulbur paralysis (Fazio-Londe disease). Indian Journal of Pediatrics. 2004 Jan; 71(1): 101-2en_US
dc.identifier.urihttps://imsear.searo.who.int/handle/123456789/84208
dc.language.isoengen_US
dc.source.urihttps://medind.nic.in/icb/icbai.shtmlen_US
dc.subject.meshBiopsy, Needleen_US
dc.subject.meshBulbar Palsy, Progressive --diagnosisen_US
dc.subject.meshChilden_US
dc.subject.meshCranial Nerves --pathologyen_US
dc.subject.meshElectromyography --methodsen_US
dc.subject.meshFemaleen_US
dc.subject.meshHumansen_US
dc.subject.meshIndiaen_US
dc.subject.meshMagnetic Resonance Imagingen_US
dc.subject.meshMotor Neurons --pathologyen_US
dc.subject.meshPrognosisen_US
dc.subject.meshRisk Assessmenten_US
dc.subject.meshSeverity of Illness Indexen_US
dc.subject.meshTomography, X-Ray Computeden_US
dc.titleProgressive bulbur paralysis (Fazio-Londe disease).en_US
dc.typeCase Reportsen_US
dc.typeJournal Articleen_US
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