Pancreatitis, polyarthritis, panniculitis syndrome’ (PPP syndrome) plus prolonged pyrexia–a rare presentation of chronic pancreatitis.
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Date
2009-09
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Abstract
Pancreatitis presenting without abdominal pain is very unusual. Here we report a 70-year-old man with chronic calcific pancreatitis presented to us with prolonged fever,
arthritis and multiple subcutaneous swellings, but without
any abdominal pain or other abdominal symptoms. His
serum amylase and lipase were very high. Biopsy from
the subcutaneous swellings revealed fat necrosis and CT
scan abdomen showed features of chronic calcific pancreatitis.
He was managed conservatively with supportive
measures, and recovered. There is only scanty information in literature regarding this type of presentation in chronic pancreatitis.
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Keywords
Amylase, fat necrosis, octreotide
Citation
Jose Tony, Biju I K, Kumar Anish, Anver P C, Kuruvila Rojan, Kuruvila Shalini, Lilly M. Pancreatitis, polyarthritis, panniculitis syndrome’ (PPP syndrome) plus prolonged pyrexia–a rare presentation of chronic pancreatitis. Indian Journal of Gastroenterology. 2009 Sept-Oct; 28(5): 186-188.