A Little More Than Just Air and Fluid: An Uncommon Case of Hydropneumothorax

Simple item page
dc.contributor.authorSengupta, Aen_US
dc.contributor.authorDutta, Sen_US
dc.date.accessioned2024-12-07T11:59:02Z
dc.date.available2024-12-07T11:59:02Z
dc.date.issued2024-03
dc.description.abstractPulmonary lymphangioleiomyomatosis (PLAM) is among one of the rarest diseases classified under diffuse parenchymal lung diseases. Sporadic LAM is extremely rare, while in patients with diagnosed tuberous sclerosis (TSC) incidence of LAM is quite high with few studies finding it in over 30–40% of TSC patients. Here we describe a case of a young female of 25 years of age presenting at a tertiary hospital in rural West Bengal, for the first time with apparently spontaneous hydropneumothorax and without any neurological features suggestive of TSC. When evaluated for the cause of hydropneumothorax, her thoracic imaging raised the suspicion of lymphangioleiomyomatosis of the lung. Thereafter she was screened for radiological and clinical features of TSC which would explain and establish her affliction with PLAM and she was eventually diagnosed as a case of PLAM associated with TSC. This underscores the importance of giving emphasis on apparently unrelated clinical findings; in this case, a papulonodular rash on her face, that may ultimately prove to be key in deciphering the underlying cause of the current clinical manifestations. Keywords: Case report, Diffuse parenchymal lung disease, Hydropneumothorax, Lymphangioleiomyomatosis, Rare interstitial lung diseases, Tuberous sclerosis, Tuberous sclerosis–lymphangioleiomyomatosisen_US
dc.identifier.affiliationsDepartment of Chest Medicine, Baruipur SD/SS Hospital, Kolkata, West Bengal, Indiaen_US
dc.identifier.affiliationsDepartment of Internal Medicine, MJN Medical College & Hospital, Cooch Behar, West Bengal, Indiaen_US
dc.identifier.citationSengupta A, Dutta S. A Little More Than Just Air and Fluid: An Uncommon Case of Hydropneumothorax. The Indian Journal of Chest Diseases and Allied Sciences. 2024 Mar; 66(1): 15–19en_US
dc.identifier.issn0377-9343
dc.identifier.placeIndiaen_US
dc.identifier.urihttps://imsear.searo.who.int/handle/123456789/242311
dc.languageenen_US
dc.publisherJaypee Brothers Medical Publishers Pvt. Ltd.en_US
dc.relation.issuenumber1en_US
dc.relation.volume66en_US
dc.source.urihttps://doi.org/10.5005/jp-journals-11007-0105en_US
dc.subjectCase reporten_US
dc.subjectDiffuse parenchymal lung diseaseen_US
dc.subjectHydropneumothoraxen_US
dc.subjectLymphangioleiomyomatosisen_US
dc.subjectRare interstitial lung diseasesen_US
dc.subjectTuberous sclerosisen_US
dc.subjectTuberous sclerosis–lymphangioleiomyomatosis.en_US
dc.titleA Little More Than Just Air and Fluid: An Uncommon Case of Hydropneumothoraxen_US
dc.typeJournal Articleen_US
Files
Original bundle
Now showing 1 - 1 of 1
No Thumbnail Available
Name:
ijcdas2024v66n1p15.pdf
Size:
1.4 MB
Format:
Adobe Portable Document Format
Download
Collections
Indian Journal of Chest Diseases & Allied Sciences