Dyke-Davidoff-Masson Syndrome: A Rare Presentation
No Thumbnail Available
Date
2024-03
Journal Title
Journal ISSN
Volume Title
Publisher
IJCP Group
Abstract
Introduction: Dyke-Davidoff-Masson syndrome (DDMS) is characterized by seizures, facial asymmetry, contralateral hemiplegia and mental retardation. The characteristic radiological features are cerebral hemiatrophy with homolateral hypertrophy of skull and sinuses. Case report: We report a case of DDMS in a 41-year-old female who presented with generalized tonic-clonic seizures, hemiparesis of the right upper and lower limb with deviation of the mouth to left. Noncontrast computed tomography (NCCT) head and magnetic resonance imaging (MRI) revealed hemiatrophy of the right cerebral hemisphere. Conclusion: DDMS is a rare disease; hence, diagnosing and managing such patients may be challenging. Our aim is to draw attention of the treating physicians towards this disease with the help of this case report.
Description
Keywords
Tonic-clonic seizures, hemiparesis, facial asymmetry, cerebral hemiatrophy, homolateral hypertrophy of skull, NCCT head
Citation
Kaur Gurdeep, Metri Rahul, Pooria Amit, Abhinav, Meena Rajesh . Dyke-Davidoff-Masson Syndrome: A Rare Presentation . Indian Journal of Clinical Practice. 2024 Mar; 34(10): 34-36