Unilateral absence of pulmonary artery: a radiographically occult cause of life-threatening hemoptysis

dc.contributor.authorAgrawal, Juhien_US
dc.contributor.authorReghunath, Anjunaen_US
dc.contributor.authorParuthi, Charuen_US
dc.contributor.authorMittal, Mahesh K.en_US
dc.contributor.authorSinha, Mukulen_US
dc.contributor.authorThukral, Brij B.en_US
dc.date.accessioned2020-11-18T10:02:12Z
dc.date.available2020-11-18T10:02:12Z
dc.date.issued2020-07
dc.description.abstractUnilateral absence or agenesis of pulmonary artery (UAPA) is a rare congenital abnormality with an estimated prevelance of 1 in 2,00,000 adults. The entity occurs commonly in association with other congenital heart diseases like septal defects or patent ductus arteriosus. The condition usually runs a benign clinical course with patients usually presenting clinically in adulthood with history of recurrent respiratory tract infections. Two such patients presented with recurrent respiratory tract infections, breathlessness and hemoptysis. The chest radiograph of first patient was reported as normal in the referring hospital, while that of second patient showed volume loss in left lung. CT Pulmonary Angiography (CTPA) was then performed which demonstrated the absence of right and left pulmonary arteries respectively in the first and second patients. Pulmonary artery branches were reformed distally by multiple collaterals arising from systemic arteries. The entire spectrum, including embryology, imaging features and management of UAPA are discussed. UAPA remains a potential cause for life-threatening hemoptysis, due to extensive collateralization associated with the condition. It is important for radiologists to be aware of this uncommon entity in order to suspect it on a routine chest radiograph, diagnose it and map associated collaterals on CTPA and also embolize the bleeding collaterals.en_US
dc.identifier.affiliationsDepartment of Radiodiagnosis, Vardhman Mahavir Medical College and Safdarjung Hospital, New Delhi, Indiaen_US
dc.identifier.citationAgrawal Juhi, Reghunath Anjuna, Paruthi Charu, Mittal Mahesh K., Sinha Mukul, Thukral Brij B.. Unilateral absence of pulmonary artery: a radiographically occult cause of life-threatening hemoptysis. International Journal of Research in Medical Sciences. 2020 Jul; 8(7): 2693-2697en_US
dc.identifier.issn2320-6071
dc.identifier.issn2320-6012
dc.identifier.placeIndiaen_US
dc.identifier.urihttps://imsear.searo.who.int/handle/123456789/212488
dc.languageenen_US
dc.publisherMedip Academyen_US
dc.relation.issuenumber7en_US
dc.relation.volume8en_US
dc.source.urihttps://dx.doi.org/10.18203/2320-6012.ijrms20202920en_US
dc.subjectComputed tomographyen_US
dc.subjectCollateralsen_US
dc.subjectEmbolizationen_US
dc.subjectHemoptysisen_US
dc.subjectPulmonary angiographyen_US
dc.subjectUnilateral agenesis of pulmonary arteryen_US
dc.titleUnilateral absence of pulmonary artery: a radiographically occult cause of life-threatening hemoptysisen_US
dc.typeJournal Articleen_US
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