Rosai Dorfman disease: a rare entity

dc.contributor.authorGoyal, Sen_US
dc.contributor.authorSharma, CMen_US
dc.contributor.authorGarg, Cen_US
dc.date.accessioned2025-08-13T11:20:12Z
dc.date.available2025-08-13T11:20:12Z
dc.date.issued2025-07
dc.description.abstractRosai Dorfman disease (RDD), a rare benign proliferative disorder of unknown etiology, stems from abnormal histiocyte accumulation within lymph node sinusoids and extra nodal tissues. While uncommon in paediatric population, RDD clinically simulates lymphoproliferative disorders. This report details a 4-year male patient presenting at a tertiary care centre with progressive bilateral cervical and submandibular lymphadenopathy lacking febrile symptoms. Diagnostic confirmation was achieved through excisional biopsy. RDD is an exclusion-based diagnosis which requires multidisciplinary collaboration and heightened clinical suspicion remains essential for paediatricians and oncologists to facilitate timely intervention and management of this rare entity.en_US
dc.identifier.affiliationsDepartment of Pediatrics, Rohilkhand Medical College and Hospital, Bareilly, Uttar Pradesh, Indiaen_US
dc.identifier.affiliationsDepartment of Pediatrics, Rohilkhand Medical College and Hospital, Bareilly, Uttar Pradesh, Indiaen_US
dc.identifier.affiliationsDepartment of Pediatrics, Rohilkhand Medical College and Hospital, Bareilly, Uttar Pradesh, Indiaen_US
dc.identifier.citationGoyal S, Sharma CM, Garg C. Rosai Dorfman disease: a rare entity. International Journal of Contemporary Pediatrics. 2025 Jul; 12(7): 1226-1228en_US
dc.identifier.issn2349-3283
dc.identifier.issn2349-3291
dc.identifier.placeIndiaen_US
dc.identifier.urihttps://imsear.searo.who.int/handle/123456789/253702
dc.languageenen_US
dc.publisherMedip Academyen_US
dc.relation.issuenumber7en_US
dc.relation.volume12en_US
dc.source.urihttps://doi.org/10.18203/2349-3291.ijcp20251880en_US
dc.subjectLymph nodesen_US
dc.subjectHistopathologyen_US
dc.subjectNon-Langerhan cellsen_US
dc.subjectSteroidsen_US
dc.titleRosai Dorfman disease: a rare entityen_US
dc.typeJournal Articleen_US
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