Reversal of severe hepato-pulmonary syndrome in congenital hepatic fibrosis after living-related liver transplantation.
| dc.contributor.author | Nagral, Aabha | en_US |
| dc.contributor.author | Nabi, Fazal | en_US |
| dc.contributor.author | Humar, Abhi | en_US |
| dc.contributor.author | Nagral, Sanjay | en_US |
| dc.contributor.author | Doctor, Nilesh | en_US |
| dc.contributor.author | Khubchandani, S R | en_US |
| dc.contributor.author | Amdekar, Y K | en_US |
| dc.date.accessioned | 2007-03-15 | en_US |
| dc.date.accessioned | 2009-05-29T03:15:24Z | |
| dc.date.available | 2007-03-15 | en_US |
| dc.date.available | 2009-05-29T03:15:24Z | |
| dc.date.issued | 2007-03-15 | en_US |
| dc.description.abstract | We report a 5-year-old girl with congenital hepatic fibrosis who presented with clubbing and cyanosis. Partial pressure of oxygen was 40 mmHg with oxy-gen saturation of 70% on room air, which improved to 128 mmHg and 92% on inhalation of 100% oxygen. Macroaggregated albumin scan showed 58% shunting to the brain, suggestive of severe hepatopulmonary syndrome. Echocardiogram and pulmonary angiogram ruled out pulmonary hypertension. Four weeks after living-related liver transplantation, she had normal blood gases and reduction in shunting to 7% on macroaggregated albumin scan. | en_US |
| dc.description.affiliation | Department of Gastroenterology, Jaslok Hospital and Research Center, Mumbai, India. nagral@vsnl.com | en_US |
| dc.identifier.citation | Nagral A, Nabi F, Humar A, Nagral S, Doctor N, Khubchandani SR, Amdekar YK. Reversal of severe hepato-pulmonary syndrome in congenital hepatic fibrosis after living-related liver transplantation. Indian Journal of Gastroenterology. 2007 Mar-Apr; 26(2): 88-9 | en_US |
| dc.identifier.uri | https://imsear.searo.who.int/handle/123456789/65122 | |
| dc.language.iso | eng | en_US |
| dc.source.uri | https://www.indianjgastro.com | en_US |
| dc.subject.mesh | Brain --radionuclide imaging | en_US |
| dc.subject.mesh | Child, Preschool | en_US |
| dc.subject.mesh | Female | en_US |
| dc.subject.mesh | Follow-Up Studies | en_US |
| dc.subject.mesh | Hepatopulmonary Syndrome --complications | en_US |
| dc.subject.mesh | Humans | en_US |
| dc.subject.mesh | Liver Cirrhosis --congenital | en_US |
| dc.subject.mesh | Liver Transplantation | en_US |
| dc.subject.mesh | Living Donors | en_US |
| dc.subject.mesh | Lung --radionuclide imaging | en_US |
| dc.subject.mesh | Technetium Tc 99m Aggregated Albumin --diagnostic use | en_US |
| dc.subject.mesh | Treatment Outcome | en_US |
| dc.title | Reversal of severe hepato-pulmonary syndrome in congenital hepatic fibrosis after living-related liver transplantation. | en_US |
| dc.type | Case Reports | en_US |
| dc.type | Journal Article | en_US |
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