Reversal of severe hepato-pulmonary syndrome in congenital hepatic fibrosis after living-related liver transplantation.

dc.contributor.authorNagral, Aabhaen_US
dc.contributor.authorNabi, Fazalen_US
dc.contributor.authorHumar, Abhien_US
dc.contributor.authorNagral, Sanjayen_US
dc.contributor.authorDoctor, Nileshen_US
dc.contributor.authorKhubchandani, S Ren_US
dc.contributor.authorAmdekar, Y Ken_US
dc.date.accessioned2007-03-15en_US
dc.date.accessioned2009-05-29T03:15:24Z
dc.date.available2007-03-15en_US
dc.date.available2009-05-29T03:15:24Z
dc.date.issued2007-03-15en_US
dc.description.abstractWe report a 5-year-old girl with congenital hepatic fibrosis who presented with clubbing and cyanosis. Partial pressure of oxygen was 40 mmHg with oxy-gen saturation of 70% on room air, which improved to 128 mmHg and 92% on inhalation of 100% oxygen. Macroaggregated albumin scan showed 58% shunting to the brain, suggestive of severe hepatopulmonary syndrome. Echocardiogram and pulmonary angiogram ruled out pulmonary hypertension. Four weeks after living-related liver transplantation, she had normal blood gases and reduction in shunting to 7% on macroaggregated albumin scan.en_US
dc.description.affiliationDepartment of Gastroenterology, Jaslok Hospital and Research Center, Mumbai, India. nagral@vsnl.comen_US
dc.identifier.citationNagral A, Nabi F, Humar A, Nagral S, Doctor N, Khubchandani SR, Amdekar YK. Reversal of severe hepato-pulmonary syndrome in congenital hepatic fibrosis after living-related liver transplantation. Indian Journal of Gastroenterology. 2007 Mar-Apr; 26(2): 88-9en_US
dc.identifier.urihttps://imsear.searo.who.int/handle/123456789/65122
dc.language.isoengen_US
dc.source.urihttps://www.indianjgastro.comen_US
dc.subject.meshBrain --radionuclide imagingen_US
dc.subject.meshChild, Preschoolen_US
dc.subject.meshFemaleen_US
dc.subject.meshFollow-Up Studiesen_US
dc.subject.meshHepatopulmonary Syndrome --complicationsen_US
dc.subject.meshHumansen_US
dc.subject.meshLiver Cirrhosis --congenitalen_US
dc.subject.meshLiver Transplantationen_US
dc.subject.meshLiving Donorsen_US
dc.subject.meshLung --radionuclide imagingen_US
dc.subject.meshTechnetium Tc 99m Aggregated Albumin --diagnostic useen_US
dc.subject.meshTreatment Outcomeen_US
dc.titleReversal of severe hepato-pulmonary syndrome in congenital hepatic fibrosis after living-related liver transplantation.en_US
dc.typeCase Reportsen_US
dc.typeJournal Articleen_US
Files
License bundle
Now showing 1 - 1 of 1
No Thumbnail Available
Name:
license.txt
Size:
1.79 KB
Format:
Plain Text
Description: