Primary Sjö-gren's syndrome presenting with distal, renal tubular acidosis and rhabdomyolysis.

Prakash, E B S; Fernando, M E; Sathiyasekaran, Malathi; Bhoopathy, R M; Jayanth, J J; Samuel, J

Primary Sjö-gren's syndrome presenting with distal, renal tubular acidosis and rhabdomyolysis.

Date

2006-12-06

Authors

Prakash, E B S

Fernando, M E

Sathiyasekaran, Malathi

Bhoopathy, R M

Jayanth, J J

Samuel, J

Abstract

Primary Sjögren's syndrome (PSS) is rare in India. Clinically manifest renal disease in PSS is uncommon and is usually an autoimmune tubulointerstitial nephritis presenting with distal renal tubular acidosis (dRTA) or a urinary concentrating defect. Hypokalemic paralysis due to dRTA in PSS is rare but well documented in medical literature. Rhabdomyolysis as a consequence of hypokalemia in PSS is exceptional. We report a case of PSS with dRTA and rhabdomyolysis causing prolonged respiratory failure and quadriparesis.

Citation

Prakash EB, Fernando ME, Sathiyasekaran M, Bhoopathy RM, Jayanth JJ, Samuel J. Primary Sjö-gren's syndrome presenting with distal, renal tubular acidosis and rhabdomyolysis. Journal of the Association of Physicians of India. 2006 Dec; 54(): 949-50