Primary haemophagocytic syndrome in a young girl.

Simple item page
dc.contributor.authorSasidharan, P K
dc.contributor.authorVarghese, Prasanth C
dc.contributor.authorSandeesp, P
dc.contributor.authorSreejith, R
dc.contributor.authorMohammed, Shaan
dc.contributor.authorShiji, P V
dc.contributor.authorSatish, H
dc.contributor.authorFeroz, M
dc.date.accessioned2012-06-25T09:19:19Z
dc.date.available2012-06-25T09:19:19Z
dc.date.issued2011-01
dc.description.abstractHaemophagocytic syndrome is a life-threatening systemic illness characterized by an uncontrolled inflammatory response. Patients present with fever, hepatosplenomegaly, jaundice and liver dysfunction, neurological manifestations and often pancytopenia. Bone marrow, lymph node, hepatic or splenic biopsy shows macrophages with ingested blood cells or their precursors. Laboratory markers include elevated triglycerides and ferritin, low fibrinogen with normal or low erythrocyte sedimentation rate (ESR). Familial haemophagocytic lymphohistiocytosis (HLH) is an autosomal recessive disorder. Secondary haemophagocytic syndrome results from infections, malignancy and collagen vascular disorders. We describe a young girl with primary haemophagocytic syndrome.en_US
dc.identifier.citationSasidharan P K, Varghese Prasanth C, Sandeesp P, Sreejith R, Mohammed Shaan, Shiji P V, Satish H, Feroz M. Primary haemophagocytic syndrome in a young girl. National Medical Journal of India. 2011 Jan-Feb; 24(1): 19-20.en_US
dc.identifier.urihttps://imsear.searo.who.int/handle/123456789/139168
dc.language.isoenen_US
dc.source.urihttps://www.nmji.in/archives/Volume-24/Issue-1/Clinical-Case-Report.pdfen_US
dc.subject.meshAdult
dc.subject.meshAmphotericin B --administration & dosage
dc.subject.meshCyclosporine --administration & dosage
dc.subject.meshDexamethasone --administration & dosage
dc.subject.meshDrug Therapy, Combination
dc.subject.meshFatal Outcome
dc.subject.meshFemale
dc.subject.meshHumans
dc.subject.meshLymphohistiocytosis, Hemophagocytic --diagnosis
dc.subject.meshLymphohistiocytosis, Hemophagocytic --drug therapy
dc.subject.meshLymphohistiocytosis, Hemophagocytic --etiology
dc.subject.meshYoung Adult
dc.titlePrimary haemophagocytic syndrome in a young girl.en_US
dc.typeArticleen_US
Files
Original bundle
Now showing 1 - 1 of 1
Thumbnail Image
Name:
nmji2011v24n1p19.pdf
Size:
57.17 KB
Format:
Adobe Portable Document Format
Description:
Journal article
Download
License bundle
Now showing 1 - 1 of 1
No Thumbnail Available
Name:
license.txt
Size:
1.71 KB
Format:
Item-specific license agreed upon to submission
Description:
Download
Collections
National Medical Journal of India