Congenital factor XIII deficiency.

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dc.contributor.authorMerchant, R Hen_US
dc.contributor.authorAgarwal, B Ren_US
dc.contributor.authorCurrimbhoy, Zen_US
dc.contributor.authorPherwani, Aen_US
dc.contributor.authorAvasthi, Ben_US
dc.date.accessioned1992-07-01en_US
dc.date.accessioned2009-05-27T04:55:28Z
dc.date.available1992-07-01en_US
dc.date.available2009-05-27T04:55:28Z
dc.date.issued1992-07-01en_US
dc.description25 references.en_US
dc.description.abstractClinical and hematological data of 9 cases with factor XIII deficiency is highlighted. The age at first bleed ranged from 3 days of life to 1 year. Seven of these 9 cases had bleeding from the umbilicus, 3 had recurrent subcutaneous and muscle hematomas, while 4 cases had CNS bleeds of which 3 expired. Routine coagulogram was normal, while clot solubility in 5 molar urea solution was abnormal in all cases. Factor XIII assay was not done in any. Patients were treated with plasma transfusion during episodes of bleeding. No patient received plasma transfusion as prophylactic therapy. The cumulative Indian data so far documented, inclusive of this series, shows a very high incidence of CNS bleeds (33%) in patients with this inherited coagulation disorder.en_US
dc.description.affiliationDivision of Neonatology, B.J. Wadia Hospital for Children, Parel, Bombay.en_US
dc.identifier.citationMerchant RH, Agarwal BR, Currimbhoy Z, Pherwani A, Avasthi B. Congenital factor XIII deficiency. Indian Pediatrics. 1992 Jul; 29(7): 831-6en_US
dc.identifier.urihttps://imsear.searo.who.int/handle/123456789/6438
dc.language.isoengen_US
dc.source.urihttps://indianpediatrics.neten_US
dc.subject.meshCerebral Hemorrhage --etiologyen_US
dc.subject.meshFactor XIII Deficiency --complicationsen_US
dc.subject.meshFemaleen_US
dc.subject.meshHumansen_US
dc.subject.meshInfanten_US
dc.subject.meshInfant, Newbornen_US
dc.subject.meshMaleen_US
dc.titleCongenital factor XIII deficiency.en_US
dc.typeCase Reportsen_US
dc.typeJournal Articleen_US
dc.typeReviewen_US
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