An unusual combination of Unilateral Orbital Plexiform Neurofibroma in a patient with oculocutaneous albinism.
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Date
2014-06
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Abstract
A 70‑year‑old female patient presented with proptosis of
right eye for the past 15 days and defective vision in both
eyes since birth. She was found to have eccentric painful
proptosis of right eye along with features of oculocutaneous
albinism. Eccentric proptosis was due to an orbital mass which
proved to be a plexiform neurofibroma by histopathological
examination. The case is presented for its rarity, as an isolated
orbital plexiform neurofibroma without the systemic features of
neurofibromatosis is rare and its coincidental presentation with
oculocutaneous albinism is yet rare and has not been reported
so far.
Description
Keywords
Oculocutaneous albinism, orbital plexiform neurofibroma, proptosis
Citation
Saravanan J,Rajendraprasad A,Priyadharshni S. An unusual combination of Unilateral Orbital Plexiform Neurofibroma in a patient with oculocutaneous albinism. Indian Journal of Ophthalmology. 2014 June ; 62 (6): 735-739.