Novel Peri-Operative Strategy for Sickle Cell Disease with Tetralogy of Fallot
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Date
2024-07
Journal Title
Journal ISSN
Volume Title
Publisher
Wolters Kluwer – Medknow
Abstract
Peri?operative management of cyanotic congenital heart disease in a patient of sickle cell disease (SCD) can be challenging. We report a case of Tetralogy of Fallot and homozygous SCD with history of multiple blood transfusions and sickle cell crises who underwent intracardiac repair. Hemoglobin S level was reduced from 75% pre?operative to 21.8% postoperative with a combination of pre?operative blood transfusion, intraoperative exchange transfusion, and normothermic cardiopulmonary bypass (CPB). Pre?operative optimization and safe intraoperative conduct were essential to avoid sickling crises.
Description
Keywords
Congenital cyanotic heart disease, exchange transfusion, sickle cell disease, sickling crisis
Citation
Khan Naveed, Dhabe Vaibhav, Kaskar Ameya, Kuppusamy Parthiban, Sen Supratim, Kumar Gaurav. Novel Peri-Operative Strategy for Sickle Cell Disease with Tetralogy of Fallot. Annals of Cardiac Anaesthesia. 2024 Jul; 27(3): 274-276