Williams?Beuren Syndrome with Pseudoaneurysm of Aortic Arch and Infective Vegetations for Modified Broms Procedure: Anesthetic Concerns & Echocardiographic Illustrations
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Date
2023-03
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Publisher
Wolters Kluwer - Medknow
Abstract
Williams?Beuren syndrome is a rare genetic malformation with predilection for supravalvular aortic stenosis. Apart from cardiovascular malformation, hypocalcemia, developmental delay, and elfin facies, challenging airway make perioperative management more eventful. Association of infective endocarditis within the aortic arch and pseudoaneurysm formation is infrequent. We, hereby report a case of pseudoaneurysm formation and infective vegetation within the aortic arch in a patient with Williams syndrome and the role of transthoracic echocardiography in its perioperative management.
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Keywords
Echocardiography, infective endocarditis, modified broms procedure, pseudoaneurysm of aortic arch, supravalvular aortic stenosis, williams?beuren syndrome
Citation
Das Devishree, Makhija Neeti. Williams?Beuren Syndrome with Pseudoaneurysm of Aortic Arch and Infective Vegetations for Modified Broms Procedure: Anesthetic Concerns & Echocardiographic Illustrations. International Journal of Medical Research & Health Sciences. 2023 Mar; 26(1): 94-96