Diagnostic Lacunae and Implications of an Automated Implantable Cardioverter Defibrillator Implantation in a Child with Type 3 Long QT (LQT3) Syndrome
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Date
2022-06
Journal Title
Journal ISSN
Volume Title
Publisher
Wolters Kluwer - Medknow
Abstract
A diagnosis of congenital long QT interval syndrome based on history and electrocardiogram was made in a child in the absence of readily available genetic testing. A genotype 3 (LQT3) was suspected after exclusion of other variants as the child was non?responsive to beta?blocker and sodium channel blocker medication. As the child continues to show episodic bradycardia, polymorphic ventricular ectopy, and T?wave alternans, a single?chamber automated implantable cardioverter?defibrillator implantation was done successfully. This report highlights how the diagnosis of LQT3 was arrived at as well as the anesthetic challenges in the management of patients with LQTS.
Description
Keywords
Anti?arrhythmia agents/administration and dosage, defibrillators, electrocardiography, implantable, long QT syndrome/diagnosis, long QT syndrome/drug therapy, voltage?gated sodium channel blockers/administration and dosage
Citation
Maddali Madan M, Kandachar Pranav S, Al?Abri Ismail A, Al?Yamani Mohammed I. Diagnostic Lacunae and Implications of an Automated Implantable Cardioverter Defibrillator Implantation in a Child with Type 3 Long QT (LQT3) Syndrome. Annals of Cardiac Anaesthesia. 2022 Jun; 25(2): 210-213