Yaranal, PJBithun, B KAnand, A S.2023-08-102023-08-102022-06Yaranal PJ, Bithun B K, Anand A S.. Primary cutaneous adenoid cystic carcinoma – An onerous task for clinicians and pathologists. Indian Journal of Pathology & Microbiology. 2022 Jun; 65(2): 459-4610377-49290974-5130http://imsear.searo.who.int/handle/123456789/223257Adenoid cystic carcinoma (ACC) is an uncommon malignant neoplasm usually confined to the salivary glands, lungs, and breasts. Primary cutaneous adenoid cystic carcinoma (PCACC) is an extremely rare entity with solitary cases reported at sites away from the scalp and chest. Hence, one must follow the multidisciplinary approach to exclude any primary ACC elsewhere in the body. We report a rare case of PCACC arising from the skin of the left lower limb in a 55-year-old woman with a history of recurrent swelling, clinically diagnosed as a metastatic tumor.Adenoid cystic carcinomaprimaryskinJournal ArticleIndiaDepartment of Pathoogy, Navodaya Medical College, Raichur, Karnataka, IndiaDepartment of Pathoogy, Kannur Medical College, Kannur, Kerala, India