Garg, AWadhera, RGulati, S PKumar, A2008-11-072009-05-302008-11-072009-05-302008-11-07Garg A, Wadhera R, Gulati SP, Kumar A. Branchio-oto-renal syndrome. Journal of the Association of Physicians of India. 2008 Nov; 56(): 904-5http://imsear.searo.who.int/handle/123456789/90034Branchio-oto-renal syndrome (Melnick-Fraser syndrome) is a rare autosomal dominant disorder characterized by syndromic association of branchial cysts or fistulae along with external, middle & inner ear malformations and renal anomalies. Authors are reporting a 19 year male patient, who presented with profound deafness & low set "lop-ear" with right sided preauricular pit. USG abdomen revealed agenesis of the left kidney.engAbnormalities, Multiple --geneticsAdultBranchio-Oto-Renal Syndrome --complicationsBranchioma --complicationsDeafness --complicationsDiagnosis, DifferentialEar --abnormalitiesHumansKidney --abnormalitiesMaleBranchio-oto-renal syndrome.Case Reports