Dahiphale, RamdasJain, ShreepalAgrawal, Mukesh2008-09-302009-05-272008-09-302009-05-272008-09-30Dahiphale R, Jain S, Agrawal M. Biotinidase deficiency. Indian Pediatrics. 2008 Sep; 45(9): 777-9http://imsear.searo.who.int/handle/123456789/12427A three month old baby presented with refractory seizures, dermatosis and persistent metabolic acidosis. Biotinidase deficiency was diagnosed on enzyme assay. Patient responded dramatically to biotin supplementation.engAcidosis --etiologyAlopecia --etiologyBiotin --therapeutic useBiotinidase Deficiency --complicationsDermatitis, Seborrheic --etiologyEpilepsy --etiologyHumansInfantMaleCase Reports