Nagarkar, RajnishRoy, ShirsenduAkheel, MohammadPalwe, VijayKulkarni, Nayana2015-07-082015-07-082014-10Nagarkar Rajnish, Roy Shirsendu, Akheel Mohammad, Palwe Vijay, Kulkarni Nayana. Rhabdomyosarcoma of Orbit: A Rare Case Report and Review. IJSS Case Reports & Reviews. 2014 Oct; 1(5): 6-10.http://imsear.searo.who.int/handle/123456789/159341Rhabdomyosarcoma (RMS) is a highly fulminant, mesenchymal malignant tumor and is considered to be one among life-threatening disease in the present decades. It is considered to be most common malignant neoplasm of the head and neck region with 10% of cases occurring in orbit. Th ough it is common in sixth and seventh decades, it can also occur in early childhood. In this article, we present a rare case of 9-yearold boy who was diagnosed with histopathologically proven RMS of orbit who had undergone a salvage left orbital exenteration following a chemotherapy. Th e main aim of this article is also to provide an overview of RMS of orbit, clinical features, investigations required, staging and various treatment modalities.enMalignant tumorNeoplasmRhabdomyosarcomaChildHumansMaleOrbit Neoplasms --diagnosisOrbit Neoplasms--pathologyOrbit Neoplasms --surgeryReview Literature as TopicRhabdomyosarcoma --diagnosisRhabdomyosarcoma -drug therapyRhabdomyosarcoma --pathologyArticle