Njie, M.Tahir, A. FadoulSidi, Boutar M.Mulendele, P. M.Haboub, M.Arous, S.Benouna, M. GhaliDrighil, A.Azouzi, L.Habbal, R.2023-07-212023-07-212022-12Njie M., Tahir A. Fadoul, Sidi Boutar M., Mulendele P. M., Haboub M., Arous S., Benouna M. Ghali, Drighil A., Azouzi L., Habbal R.. Acute Aortic Dissection Masquerading a Rare Type of Congenital Bicuspid Aortic : A Case Report. Cardiology and Angiology: An International Journal. 2022 Dec; 11(4): 430-4362347-520Xhttp://imsear.searo.who.int/handle/123456789/220232Acute aortic dissection on bicuspid aortic valve (BAV) type 0 is a rare especially in young masculine. Risk factors like smoking and intensive sport activities can hasten their apparition especially in non-diagnosed population. Trans thoracic echocardiography is very important in the diagnosis of BAV whereas Angio CT scan helps to confirm acute aortic dissection. Treatment is based on surgery for type A Stanford classification for acute aortic dissection. We report a rare case of acute aortic dissection masquerading a rare type of BAV, type 0 in a young sportive male with no history of heart disease who presented for the first-time with acute chest pain after lifting a heavy weight metal at the complex sport center. Patient was initially placed on medical treatment before surgery for heart valve and root replacement (Bentall procedure).Aorticbicuspid aortic valveheart disease.Journal ArticleIndiaDepartment of Cardiology P37, Ibn Rochd University Hospital, Casablanca, MoroccoFaculty of Medicine and Pharmacy, Hassan II University of Casablanca, Casablanca, Morocco