Gayathri, Amonkar PJaya, Deshpande RAnjali, Amarapurkar DArti, Karpate2007-10-012009-05-292007-10-012009-05-292007-10-01Gayathri AP, Jaya DR, Anjali AD, Arti K. Portopulmonary hypertension in a case of non-cirrhotic portal fibrosis. Indian Journal of Pathology & Microbiology. 2007 Oct; 50(4): 828-30http://imsear.searo.who.int/handle/123456789/74815Portopulmonary hypertension (PPHT) is the unusual association of portal hypertension (HT) with pulmonary HT. We report a case of noncirrhotic portal fibrosis (NCPF) leading to PPHT which is exceedingly rare with only very few cases reported in the literature. This is an autopsy report of a 30 years old man, a known case of portal HT who died suddenly due to a syncopal attack. Autopsy revealed massive pulmonary thromobembolism with pulmonary HT. Liver showed changes of NCPF. The rarity of NCPF causing PPHT prompted this case report.engAdultAutopsyFatal OutcomeHumansHypertension, Portal --complicationsHypertension, Pulmonary --complicationsLiver Cirrhosis --pathologyMalePulmonary Embolism --diagnosisSyncopeCase Reports