Subramaniam, PMathew, SSugnani, S N2008-04-082009-06-022008-04-082009-06-022008-04-08Subramaniam P, Mathew S, Sugnani SN. Dentinogenesis imperfecta: A case report. Journal of the Indian Society of Pedodontics and Preventive Dentistry. 2008 Apr-Jun; 26(2): 85-7http://imsear.searo.who.int/handle/123456789/115057Dentinogenesis imperfecta is an autosomal dominant disorder of tooth development characterized by the presence of opalescent dentin, resulting in a dusky blue to brownish discoloration of the teeth. This condition is genetically and clinically heterogeneous; it may affect only the teeth or it may be associated with the osteogenesis imperfecta. Dentinogenesis imperfecta has been subdivided into three types: type I is associated with osteogenesis imperfecta; in type II there is no associated osteogenesis imperfecta; and when the condition is associated with the Brandywine triracial isolate and large pulp chambers it is classified as type III. This report describes a 16-year-old female patient who showed the characteristic dental features of dentinogenesis imperfecta type II. The etiology and prevalence of the disorder, and a comprehensive treatment plan, will be briefly reviewed.engJournal Article