Majumder, ASen, D2020-04-102020-04-102019-09Majumder A, Sen D. Kimura disease with nephrotic syndrome in a child- A rare association. Indian Journal of Pathology and Microbiology. 2019 Sep; 62(3): 437-4400377-49290974-5130http://imsear.searo.who.int/handle/123456789/196367Lymphadenopathy along with various systemic manifestations is commonly encountered in pediatric patients, tuberculosis being the commonest etiology. Occasional patients may present a diagnostic conundrum. Here, the authors report an unusual manifestation of Kimura disease (KD) presenting as nephrotic syndrome associated with mesenteric lymphadenitis in an 11-year-old male child. KD is a chronic inflammatory disorder of unknown etiology. It typically affects young adult males in the age range of 27-40 years and usually presents as painless itchy nodular masses in the head and neck region. The involvement of mesenteric lymph nodes along with a very young age of presentation makes it a rare case, posing a diagnostic challenge for the unsuspecting physician.Angiolymphoid hyperplasia with eosinophilia (ALHE)IgG4-related diseaseKimura diseasenephrotic syndromeKimura disease with nephrotic syndrome in a child- A rare associationJournal ArticleIndiaDepartment of Pathology, Military Hospital Jodhpur, Jodhpur, Rajasthan, IndiaDepartment of Radiodiagnosis and Imaging, Command Hospital, Pune, Maharashtra, India