Christopher, RRajivnath, VShetty, K T1997-03-012009-05-301997-03-012009-05-301997-03-01Christopher R, Rajivnath V, Shetty KT. Arginase deficiency. Indian Journal of Pediatrics. 1997 Mar-Apr; 64(2): 266-9http://imsear.searo.who.int/handle/123456789/83492Hyperargininemia due to arginase deficiency is a rare, inherited, urea cycle disorder. We report a case of arginase deficiency in a 5-year old boy presenting with mild hyperammonemia, hyperargininemia, and dibasic aminoaciduria.engArginase --deficiencyChild, PreschoolChromosome Aberrations --geneticsChromosome DisordersGenes, RecessiveHumansHyperargininemia --diagnosisMaleArginase deficiency.Case Reports