Rao, V Arun PrasadReddy, N VenugopalKrishana, RSugumaran, D KPallavi, PandeyPari, Arul2016-02-222016-02-222010-04Rao V Arun Prasad. Reddy N Venugopal, Krishana R, D K Sugumaran, Pallavi Pandey, Pari Arul. Hypohydrotic ectodermal dysplasia -a case report .Annals and Essences of Dentistry. 2010 Apr-June; 2(2): 31-35.0975-8798http://imsear.searo.who.int/handle/123456789/173795Ectodermal dysplasia is a rare hereditary disorder. Its Hypohidrotic (HED) variant is also known as Chirst- Siemens-Touraine syndrome. It is inherited as an X- linked trait. Such Patients are characterized by the clinical manifestations of Hypodontia, Hypotrichosis, Hypohidrosis and a highly characteristic facial physiognomy. This article, reports a typical case of Hypohidrotic Ectodermal Dysplasia (HED) and management.enEctodermal dysplasiaHypohidrotic ectodermal dysplasiaHypodontiaHypotrichosiArticle