ehrotra, BBhargav, MKapoor, APandey, SBrij, SGopal, VR2025-06-192025-06-192025-03ehrotra B, Bhargav M, Kapoor A, Pandey S, Brij S, Gopal VR. Papillary glioneuronal tumor: A rare case with recent updates as per 2021 CNS WHO 5th classification. Indian Journal of Pathology & Microbiology. 2025 Mar; 68(1): 180-1820377-49290974-5130https://imsear.searo.who.int/handle/123456789/249948The papillary glioneuronal tumor is a WHO grade 1, rare neuronal?glial tumor and comprises 0.02% of all CNS tumors. Histologically, it is a mixture of glial and neuronal components showing a pseudopapillary pattern with hyalinized vessels. PGNT is considered a low?grade neoplasm, and surgical excision has been curative in most cases. In this paper, we report a new case of papillary glioneuronal tumor in a 44?year?old male having a divergent presentation, to analyze it due to the rarity of its occurrence as per the latest classification.Frontal lobeglioneuronal tumormiddle agepapillaryJournal ArticleIndiaMD Pathology, RML Laboratory, Lucknow, Uttar PradeshMD Pathology, RML Laboratory, Lucknow, Uttar PradeshMD Pathology, RML Laboratory, Lucknow, Uttar PradeshMD Pathology, RML Laboratory, Lucknow, Uttar PradeshMD Pathology, RML Laboratory, Lucknow, Uttar PradeshMS Surgery, RMLIMS, Lucknow, Uttar Pradesh, India