Kulkarni, Maithili MandarKhandeparkar, Siddhi Gaurish SinaiJoshi, Avinash RBhayekar, Pallavi V2016-12-102016-12-102016-10Kulkarni Maithili Mandar, Khandeparkar Siddhi Gaurish Sinai, Joshi Avinash R, Bhayekar Pallavi V. Unilateral gonadoblastoma with dysgerminoma in normal fertile woman having a child: Extremely rare occurrence with characteristic immunohistomorphology. Indian Journal of Pathology & Microbiology. 2016 Oct-Dec 59(4): 527-529.http://imsear.searo.who.int/handle/123456789/179673Gonadoblastomas (GBYs) are rare gonadal tumors almost always arising from a dysgenetic gonad with a Y chromosome. Very rarely, GBYs appear in otherwise normal women with a history of pregnancy. The typical histological appearance of GBY can be altered by extensive deposition of basement membrane material, calcification, or overgrowth by a malignant tumor. Less than 10 cases have been reported with normal 46XX karyotype. Only six cases of GBY have been described in pregnant women. We present a unique case of GBY with dysgerminoma in a genotypically and phenotypically normal woman with a history of normal pregnancy, absence of virilization, and characteristic immunohistomorphological features.enFertile womangonadoblastoma with dysgerminomagonadoblastoma with normal karyotypeArticle