Maddali, Madan MKandachar, Pranav SAl?Abri, Ismail AAl?Yamani, Mohammed I2023-07-142023-07-142022-06Maddali Madan M, Kandachar Pranav S, Al?Abri Ismail A, Al?Yamani Mohammed I. Diagnostic Lacunae and Implications of an Automated Implantable Cardioverter Defibrillator Implantation in a Child with Type 3 Long QT (LQT3) Syndrome. Annals of Cardiac Anaesthesia. 2022 Jun; 25(2): 210-2130974-51810971-9784http://imsear.searo.who.int/handle/123456789/219212A diagnosis of congenital long QT interval syndrome based on history and electrocardiogram was made in a child in the absence of readily available genetic testing. A genotype 3 (LQT3) was suspected after exclusion of other variants as the child was non?responsive to beta?blocker and sodium channel blocker medication. As the child continues to show episodic bradycardia, polymorphic ventricular ectopy, and T?wave alternans, a single?chamber automated implantable cardioverter?defibrillator implantation was done successfully. This report highlights how the diagnosis of LQT3 was arrived at as well as the anesthetic challenges in the management of patients with LQTS.Anti?arrhythmia agents/administration and dosagedefibrillatorselectrocardiographyimplantablelong QT syndrome/diagnosislong QT syndrome/drug therapyvoltage?gated sodium channel blockers/administration and dosageJournal ArticleIndiaDepartments of Cardiac AnesthesiaCardiothoracic Surgery andPediatric Cardiology, National Heart Center, Royal Hospital, Muscat, Sultanate of Oman