A Case of Arrhythmogenic Right Ventricular Cardiomyopathy with Left Ventricular Involvement Presenting as Recurrent Ventricular Tachycardia
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Date
2025-05
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Indian Medical Association
Abstract
Background : Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) is condition of genetic inheritance. Pathologically characterized by fibrofatty replacement of cardiac muscle mainly in right ventricular myocardium. Ventricular arrhythmias of right ventricular origin may lead to sudden cardiac death in young adults and athletes. Usually, male patients with age less than 40 years present with recurrent palpitation later develop progressive right heart or biventricular failure. Here we report a case of Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) with left ventricular involvement with recurrent ventricular tachycardia. Case Presentation : A 39-year-old male patient with no comorbidities presented with palpitations and giddiness. He was hemodynamically unstable and ECG showed ventricular tachycardia with Left Bundle Branch Black (LBBB) morphology. Patient was managed with cardioversion and anti arrhythmic drugs amiodarone and betablockers. His 2D echo and cardiac MRI done and diagnosis of arrhythmogenic right ventricular cardiomyopathy with left ventricular involvement was made based on 2020 international criteria. He was adviced Implantable Cardioverter-Defibrillator (ICD) implantation. As patient refused ICD implantation he was continued on amiodarone and beta blockers. Conclusions : ARVC is a rare disorder, and proper diagnosis is important to avoid unnecessary delay in managing the patients. 2020 International criteria helps to diagnose ARVC. Although ICD implantation is the treatment of choice for these patients, medical management with beta-blockers and amiodarone are helpful to prevent recurrent episodes of ventricular tachycardia in these patients.
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Keywords
Arrhythmogenic Right Ventricular Cardiomyopathy, Recurrent Ventricular Tachycardia, LV Involvement
Citation
Chigullapalli S, Sharma V. A Case of Arrhythmogenic Right Ventricular Cardiomyopathy with Left Ventricular Involvement Presenting as Recurrent Ventricular Tachycardia. Journal of The Indian Medical Association. 2025 May; 123(5): 57-58