Type I Dentinal Dysplasia—Proposal of A New Classification System Combined with A Variant Case Presentation
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Date
2014-02
Journal Title
Journal ISSN
Volume Title
Publisher
Association of Medical Dental and Allied Sciences
Abstract
Dentine dysplasia is an extremely rare autosomal dominant hereditary condition primarily characterized by defective dentine formation affecting both the deciduous and permanent dentitions. The aetiology of dentinal dysplasia remains imprecise to date, in spite of the numerous hypotheses put forward by various authors. Also, of late, new case reports of type I dentine dysplasias are emerging with clinical and radiographic findings which are unique and variant from the classical characteristic features of this anomaly, rendering it difficult to fit into the previously established classification systems. In this article, after a thorough review and understanding of the drawbacks of the previous classification systems and the cumulative findings from the published case reports in literature, we propose a new classification system for dentine dysplasia type I. We also present a case report which exhibited an absence of familial hereditary pattern, the absence of periradicular radiolucent lesions and osseous pathologies as well as atypical morphological defects of the molar roots which were diverse from the classical findings of the various sub types of dentine dysplasia type I reported to date. Early diagnosis and implementation of preventive and curative therapy is crucial for avoiding premature exfoliation of deciduous and permanent dentition and associated residual ridge resorption, thereby overcoming functional and aesthetic deficits. The new classification proposed in this article will help clinicians to diagnose and categorize the patients effectively, facilitating proper treatment and supportive care for all.
Description
Keywords
Classification systems, Dentine dysplasia, Radiograph, Periradicular lesions, Dental papilla
Citation
Nettem Sowmya, S Venkatachalapathi, Nettemu Sunil Kumar, K Kameswari, Pendyala Siva Kumar. Type I Dentinal Dysplasia—Proposal of A New Classification System Combined with A Variant Case Presentation. Indian Journal of Mednodent and Allied Sciences. 2014 Feb; 2(1): 109-114