Macroorchidism: Consequence of Untreated Congenital Adrenal Hyperplasia.

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Date
2012-07
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Abstract
Testicular adrenal rest tumors (TART) are consequences of delayed diagnosis and/or undertreatment in patients with congenital adrenal hyperplasia (CAH). We describe a case of CAH with TART who presented with bilateral macroorchidism. He was managed with glucocorticoids which led to decrease in testicular size without restoration of spermatogenesis.
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Keywords
Congenital adrenal hyperplasia, Macroorchidism, Testicular adrenal rest tumors
Citation
Rastogi Ashu, Walia Rama, Saikia Uma Nahar, Bhansali Anil. Macroorchidism: Consequence of Untreated Congenital Adrenal Hyperplasia. Indian Pediatrics. 2012 July; 49(7): 577-578.