Hepatopulmonary syndrome, an unusual cause of hypoxemia.
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2007-12-05
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Abstract
A six-year-old boy presented with cough, cyanosis and clubbing. Investigations revealed hypoxia (PaO2 53 mm Hg on room air) which was only partially correctable (PaO2 73 mm Hg) with 100% oxygen administered through a non re breathing face mask. Liver function tests showed elevated total bilirubin, and transaminases, liver biopsy confirmed chronic hepatitis and endoscopy showed grade three varices. A contrast enhanced echocardiography (bubble study) revealed pulmonary arterio-venous communication. A diagnosis of hepatopulmonary syndrome was made based on the triad of hypoxemia, liver disease and intra pulmonary vascular communications.
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Sindhu S, Ramesh P, Juneja R, Kabra SK. Hepatopulmonary syndrome, an unusual cause of hypoxemia. Indian Journal of Pediatrics. 2007 Dec; 74(12): 1127-9