Sinus histiocytosis with massive lymphadenopathy: complicated by autoimmune hemolytic anemia.

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2003-09-19
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Abstract
Sinus histiocytosis with massive lymphadenopathy is a rare histiocytic disorder with very few case reports in Indian literature. Immunological abnormalities have been documented in few cases. We report one such case of a child presenting with generalized lymphadenopathy and complicated by autoimmune hemolytic anemia, suggestive of an associated immune dysfunction.
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Kiran PS, Sowdi VP, Shetty SB, Venugopal U, Parameshwariah S, Dias E, Kamala CS. Sinus histiocytosis with massive lymphadenopathy: complicated by autoimmune hemolytic anemia. Indian Journal of Pediatrics. 2003 Sep; 70(9): 759-60