Wunderlich's syndrome with hepatic angiomyolipoma in tuberous sclerosis.

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Date
2008-04-16
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Abstract
We present a patient of tuberous sclerosis complex with bilateral renal angiomyolipoma and hepatic angiomyolipoma with spontaneous retroperitoneal hemorrhage from right angiomyolipoma (Wunderlich's syndrome). Nephron preserving approach was tried but the right kidney could not be salvaged. Hepatic angiomyolipoma was managed conservatively. Wunderlich's syndrome has been found in around 10% of cases of renal angiomyolipomas. Hepatic Angiomyolipoma is a benign mesenchymal neoplasm of the liver which is rarely reported in literature.
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Mongha R, Bansal P, Dutta A, Das RK, Kundu AK. Wunderlich's syndrome with hepatic angiomyolipoma in tuberous sclerosis. Indian Journal of Cancer. 2008 Apr-Jun; 45(2): 64-6
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https://imsear.searo.who.int/handle/123456789/50255
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Indian Journal of Cancer