Biphenotypic sinonasal sarcoma—A recently described entity with many mimics: A case report
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Date
2023-06
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Publisher
Wolters Kluwer - Medknow
Abstract
Biphenotypic sinonasal sarcoma (BSNS) is a recently described, low-grade, slow-growing sarcoma with neural and myogenic features with exclusive location in sinonasal track and characteristic PAX3- MAML3 gene fusion. Differentiating this tumor from its commoner mimics needs knowledge of this entity to avoid over treatment. This tumor has unique morphology, clinical course, and genetics. We report this in a 47-year-old female who was diagnosed with such a rare, solitary fibrous tumor—hemangiopericytoma (HPC-SFT) on limited initial biopsy. On subsequent excision, typical morphology and immunohistochemistry helped to clinch the diagnosis.
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Keywords
Biphenotypic sinonasal sarcoma, BSNS, low-grade sinonasal sarcoma with neural and myogenic features, PAX3 gene, sinonasal sarcoma
Citation
Ingle A, Mahendra N, Gopal Reddy G V.. Biphenotypic sinonasal sarcoma—A recently described entity with many mimics: A case report. Indian Journal of Pathology & Microbiology. 2023 Jun; 66(2): 396-399