Pediatric primary extra-ovarian Sertoli Leydig cell tumor of the retroperitoneum

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Date
2023-03
Journal Title
Journal ISSN
Volume Title
Publisher
Wolters Kluwer - Medknow
Abstract
Ovarian Sertoli Leydig cell tumors (SLCT) accounts for less than 0.5% of all ovarian malignancies. The incidence of primary extra-ovarian SLCT is extremely rare with reported cases occurring in young adult women till now. We report case of primary retroperitoneal extra-ovarian SLCT in a seven-year girl child without any hormonal manifestation. She presented with complaint of left side abdominal swelling associated with intermittent pain for a duration of six months. CT scan revealed a huge retroperitoneal space-occupying lesion abutting the dorsal vertebrae and present posterior to pancreas, spleen and left kidney. The tumor was diagnosed as extraovarian Sertoli Leydig cell tumor with intermediate differentiation on histopathology and immunohistochemistry.
Description
Keywords
Gonadal ridge, inhibin, retroperitonium, sertoli-leydig cell tumor, sex cord cell
Citation
Panigrahi C, Mishra P, Pati AB, Das K, Sable M.. Pediatric primary extra-ovarian Sertoli Leydig cell tumor of the retroperitoneum. Indian Journal of Pathology & Microbiology. 2023 Mar; 66(1): 145-147