Recurrent intestinal obstruction in a patient of Peutz–Jeghers syndrome
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Date
2019-01
Journal Title
Journal ISSN
Volume Title
Publisher
Wolters Kluwer India Pvt. Ltd.
Abstract
Peutz–Jeghers syndrome is a rare hamartomatous polyposis syndrome characterized by the presence of intestinal polyps and mucocutaneous melanotic pigmentations. It is associated with various gastrointestinal and extraintestinal malignancies. This case report deals with the clinical presentation, investigations, operative findings, and outcome of a patient harboring this disease. A 45-year-old female presented to us with intermittent colicky abdominal pain for the last 6 months and a single episode of melena 1 month back. She had a previous history of resection of a jejunal growth 22 years back. The histopathology report was suggestive of papillary adenocarcinoma. On examination, hyperpigmented macules were seen on her lips and buccal mucosa. Laparotomy revealed multiple polyps mainly in the proximal small intestine and a focus of ileoileal intussusception. A limited resection was done
Description
Keywords
Intestinal hamartomatous polyps, mucocutaneous hyperpigmented macules, Peutz–Jeghers syndrome, small intestinal adenocarcinoma
Citation
Kumar Sundeep, Arora Preeti, Goswami Pabitra. Recurrent intestinal obstruction in a patient of Peutz–Jeghers syndrome. Journal of Cancer Research and Therapeutics. 2019 Jan; 15(1): 252-254