Movement Disorder Early in the Presentation of Two Children with Subacute Sclerosing Pan-Encephalitis
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Date
2019-04
Journal Title
Journal ISSN
Volume Title
Publisher
SCIENCEDOMAIN international
Abstract
Subacute sclerosing panencephalitis(SSPE) is a progressive degenerative disease caused by measles infection with overall poor prognosis in spite multiple modalities of treatment. The course of the disease is characterized by progressive neurological decline in the form of behavioral and personality changes followed by a stage of characteristic periodic myoclonic spasms followed by a stage of quadriplegia movement disorder, vegetative state and frequently early death. Here we report two cases with atypical presentation of early rather than late movement disorder during illness and the unusual association of central precocious puberty preceding the course of illness in one of the cases
Description
Keywords
Subacute sclerosing panencephalitis, prognosis, myoclonicspasms, quadriplegia movement disorder, central precocious puberty.
Citation
Al-Gethami Hanin, Alrifai Mohammad Talal, Al-Rumayyan Ahmed, Waleed Al-Tuwaijri, Duaa Ba-Armah. Movement Disorder Early in the Presentation of Two Children with Subacute Sclerosing Pan-Encephalitis. International Neuropsychiatric Disease Journal. 2019 Apr; 13(1): 1-10