Solitary orbital myofibroma in a child: A rare case report with literature review
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Date
2019-07
Authors
Journal Title
Journal ISSN
Volume Title
Publisher
All India Ophthalmological Society
Abstract
Myofibroma is a rare benign mesenchymal tumor of uncertain histogenesis. A six-year-old boy presented with a unilateral lower eyelid mass of six weeks' duration. MRI revealed a circumscribed mass in the inferolateral orbit with bony erosion. A systemic examination was unremarkable. Excision with histopathology revealed a partially infiltrative spindle cell tumor with bland nuclear morphology expressing smooth muscle actin and muscle-specific actin, compatible with myofibroma. Solitary myofibroma is a rare childhood orbital tumor and may clinico-radiologically closely mimic a malignancy. Histopathology and immunohistochemistry can help reach a definitive diagnosis. Systemic evaluation and close follow up are crucial in such cases.
Description
Keywords
Benign, bone erosion, children, myofibromatosis, orbital myofibroma
Citation
Madhuri BK, Tripathy D, Mittal R. Solitary orbital myofibroma in a child: A rare case report with literature review. Indian Journal of Ophthalmology. 2019 Jul; 67(7): 1240-1245