Kimura disease with nephrotic syndrome in a child- A rare association
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Date
2019-09
Authors
Journal Title
Journal ISSN
Volume Title
Publisher
Indian Association of Pathologists and Microbiologists
Abstract
Lymphadenopathy along with various systemic manifestations is commonly encountered in pediatric patients, tuberculosis being the commonest etiology. Occasional patients may present a diagnostic conundrum. Here, the authors report an unusual manifestation of Kimura disease (KD) presenting as nephrotic syndrome associated with mesenteric lymphadenitis in an 11-year-old male child. KD is a chronic inflammatory disorder of unknown etiology. It typically affects young adult males in the age range of 27-40 years and usually presents as painless itchy nodular masses in the head and neck region. The involvement of mesenteric lymph nodes along with a very young age of presentation makes it a rare case, posing a diagnostic challenge for the unsuspecting physician.
Description
Keywords
Angiolymphoid hyperplasia with eosinophilia (ALHE), IgG4-related disease, Kimura disease, nephrotic syndrome
Citation
Majumder A, Sen D. Kimura disease with nephrotic syndrome in a child- A rare association. Indian Journal of Pathology and Microbiology. 2019 Sep; 62(3): 437-440