A case of febrile ulceronecrotic Mucha-Habermann disease with comorbidities

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Date
2019-11
Journal Title
Journal ISSN
Volume Title
Publisher
Indian Association of Dermatologists, Venereologists & Leprologists
Abstract
Febrile ulceronecrotic Mucha-Habermann disease is a very rare and severe variant of pityriasis lichenoides et varioliformis acuta. Adult cases are difficult to diagnose as in the early course they can mimic erythema multiforme or lymphomatoid papulosis. We report a case of a 38-year-old woman who presented with 90% body surface area involvement, fever, diarrhea, malaise and associated comorbidities. She was treated with systemic steroids and methotrexate but suffered a fatal outcome. So far, a total of 65 cases are reported in the literature.
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Keywords
Dermatologic emergencies, febrile ulceronecrotic Mucha‑Habermann disease, pityriasis lichenoides et varioliformis acuta
Citation
Bhide Dhanashree Santosh, Tulpule Mukta Shriram, Pethe Suresh V. A case of febrile ulceronecrotic Mucha-Habermann disease with comorbidities. Indian Journal of Dermatology, Venereology and Leprology. 2019 Nov; 85(6): 660-663