Multiple Fibroids in a Case of MRKH Syndrome with Absent Uterus: Recommendations for Management.
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Date
2014-02
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Abstract
Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is a rare congenital anomaly characterized by aplasia or hypoplasia of
uterus and vagina in women with normal development of secondary sex characteristics. It affects one in 4,000-5,000 female
births. Women with this syndrome present in their teens with primary amenorrhea. MRKH syndrome may be associated with
renal, skeletal, cardiac and auditory anomalies. Although, very rare women with MRKH syndrome may develop leiomyomas
from a rudimentary uterus. Initial investigation in women having MRKH syndrome with leiomyoma is ultrasonography (USG).
However, magnetic resonance imaging (MRI) is more accurate for diagnosis. Complete removal of the masses with the uterine
remnant is recommended.
Description
Keywords
MRKH syndrome,, leiomyoma, MRI, laparotomy
Citation
Valecha Shalini Mahana, Katdare Prajakta, Kargar Uday, Shende Prajakta. Multiple Fibroids in a Case of MRKH Syndrome with Absent Uterus: Recommendations for Management. Indian Journal of Clinical Practice. 2014 Feb; 24(9): 856-858.