Isolated ileal ganglioneuromatosis in an 11‑year‑old boy: Case report and review of literature.
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Date
2016-07
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Abstract
Ganglioneuromatous proliferation in the gastrointestinal tract is a rare occurrence
and is usually associated with specific syndrome complexes such as multiple
endocrine neoplasia Type 2B or von Recklinghausen’s disease. We report
here a case of diffuse intestinal ganglioneuromatosis, presenting as intestinal
obstruction and chronic constipation in an 11‑year‑old boy. Sporadic cases of
intestinal ganglioneuromatosis in the absence of any systemic manifestations
are a very rare cause of enteric motility disorders in childhood, and we discuss
the pathological and clinical significance of this finding. Histopathological
identification of this uncommon cause of a common pediatric problem is important
since the condition is amenable to surgical treatment.
Description
Keywords
Diffuse, ganglioneuromatosis, intestinal, isolated
Citation
Mitra Subhashis, Mukherjee Sanghamitra, Chakraborty Hema. Isolated ileal ganglioneuromatosis in an 11‑year‑old boy: Case report and review of literature. Indian Journal of Pathology & Microbiology. 2016 July-Sept 59(3): 365-367.